Sickle cell anemia is a severe hemolytic anemia that results from inheritance of the sickle hemoglobin gene. Show
What is Sickle Cell Anemia?Sickle cell anemia is an inherited form of hemolytic anemia.
PathophysiologyThe HbS gene causes the hemoglobin molecule to be defective. Normal RBC vs Sickled RBC
CausesThe causes of sickle cell anemia include:
Clinical ManifestationsSymptoms of sickle cell anemia vary and are only somewhat based on the amount of HbS.
ComplicationsComplications of sickle cell anemia include:
Assessment and Diagnostic FindingsThe patient with sickle cell anemia usually has the following laboratory results:
Medical ManagementTreatment for sickle cell anemia is the focus of continued research.
Pharmacologic Therapy
Nursing ManagementNursing management for a patient with sickle cell anemia focus on the following: Nursing AssessmentAssessment data for a sickle cell anemia patient should include:
Nursing DiagnosisBased on the assessment data, major nursing diagnosis for the patient include:
Nursing Care Planning and GoalsMain Article: 6 Sickle Cell Anemia Crisis Nursing Care Plans The major goals for the patient are:
Nursing InterventionsNursing interventions for sickle cell anemia include: Managing Pain
Preventing and Managing Infection
Promoting Coping Skills
Increasing Knowledge
Monitoring and Managing Potential Complications
LEG ULCERS
PRIAPISM LEADING TO IMPOTENCE
CHRONIC PAIN AND SUBSTANCE ABUSE
Promoting Home and Community Based Care
EvaluationExpected patient outcomes are:
Discharge and Home Care GuidelinesEducation is always the best way to impart what the patient and the family need to know for home care.
Documentation GuidelinesThe focus of documentation in a patient with sickle cell anemia include:
Practice Quiz: Sickle Cell AnemiaHere’s a 5-item quiz about the study guide. Please visit our nursing test bank page for more NCLEX practice questions. 1. A nurse expects an adult patient with sickle cell anemia to have a hemoglobin value of: A. Near 3 g/dl. 2. Sickle-shaped erythrocytes cause: A. Cellular blockage in small vessels. 3. A person with sickle cell trait would: A. Be advised to avoid fluid loss and dehydration. 4. On the basis of the knowledge of the inheritance of the sickle cell gene, the nurse expects the patient to be of what descent? A. African. 5. On assessment, the nurse notes that the patient’s face and skull bones are enlarged. She knows this is a compensatory response to: A. Dehydration. Answers and Rationale 1. Answer: D. Between 7 and 10 g/dl. A patient with sickle cell anemia has a hemoglobin level of between 7 and 10 g/dl. 2. Answer: D. All of the above.
3. Answer: B. Be protected from crisis under ordinary circumstances.
4. Answer: A. African.
5. Answer: B. Anemia. The bones are enlarged as compensatory response to offset anemia. See AlsoPosts related to this care plan:
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